Weaning practices in phenylketonuria vary between health professionals in Europe


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Pinto A., Adams S., Ahring K., Allen H., Almeida M. F. , Garcia-Arenas D., et al.

MOLECULAR GENETICS AND METABOLISM REPORTS, cilt.18, ss.39-44, 2019 (SCI İndekslerine Giren Dergi) identifier identifier identifier

  • Cilt numarası: 18
  • Basım Tarihi: 2019
  • Doi Numarası: 10.1016/j.ymgmr.2018.11.003
  • Dergi Adı: MOLECULAR GENETICS AND METABOLISM REPORTS
  • Sayfa Sayısı: ss.39-44

Özet

Background: In phenylketonuria (PKU), weaning is considered more challenging when compared to feeding healthy infants. The primary aim of weaning is to gradually replace natural protein from breast milk or standard infant formula with solids containing equivalent phenylalanine (Phe). In addition, a Phe-free second stage L-amino acid supplement is usually recommended from around 6 months to replace Phe-free infant formula. Our aim was to assess different weaning approaches used by health professionals across Europe.