Weaning practices in phenylketonuria vary between health professionals in Europe


Creative Commons License

Pinto A., Adams S., Ahring K., Allen H., Almeida M. F. , Garcia-Arenas D., ...More

MOLECULAR GENETICS AND METABOLISM REPORTS, vol.18, pp.39-44, 2019 (Journal Indexed in SCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 18
  • Publication Date: 2019
  • Doi Number: 10.1016/j.ymgmr.2018.11.003
  • Title of Journal : MOLECULAR GENETICS AND METABOLISM REPORTS
  • Page Numbers: pp.39-44

Abstract

Background: In phenylketonuria (PKU), weaning is considered more challenging when compared to feeding healthy infants. The primary aim of weaning is to gradually replace natural protein from breast milk or standard infant formula with solids containing equivalent phenylalanine (Phe). In addition, a Phe-free second stage L-amino acid supplement is usually recommended from around 6 months to replace Phe-free infant formula. Our aim was to assess different weaning approaches used by health professionals across Europe.