Scimitar Syndrome associated with partial anomalous pulmonary venous draining into superior vena cava


DEMİR E. , ASKIN M., MIDYAT L., GÜLEN F. , Ulger Z. , TANAC R., ...More

EUROPEAN JOURNAL OF PEDIATRICS, vol.169, no.10, pp.1263-1265, 2010 (Journal Indexed in SCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 169 Issue: 10
  • Publication Date: 2010
  • Doi Number: 10.1007/s00431-010-1153-3
  • Title of Journal : EUROPEAN JOURNAL OF PEDIATRICS
  • Page Numbers: pp.1263-1265

Abstract

Scimitar syndrome is a rare congenital cardiopulmonary malformation characterized by hypoplasia of the right lung and drainage of the right pulmonary veins into the vena cava inferior. It may also be associated with cardiac dextroversion and anomalies of the tracheobronchial system, cardiovascular system, and diaphragm. Some cases are asymptomatic with others diagnosed in early-childhood period with pulmonary hypoplasia and other associated malformations. We present here a patient whose venous return of the middle and lower lobes of the right lung is into the superior vena cava, which is a very unusual finding for this disorder.