Escobar multiple pterygium sendromu Çok nadir bir sendroma multidisipliner yaklaşım


SÖZBİLEN M. C. , GÜNAY H. , ÇALIŞ F.

24. ULUSAL ORTOPEDİ VE TRAVMATOLOJİ KONGRESİ, Antalya, Turkey, 27 - 30 November 2014, vol.27, pp.171-174 identifier identifier identifier

  • Publication Type: Conference Paper / Full Text
  • Volume: 27
  • Doi Number: 10.5606/ehc.2016.34
  • City: Antalya
  • Country: Turkey
  • Page Numbers: pp.171-174

Abstract

Escobar (multiple pterygium) syndrome is progressive and a very rare syndrome. It is generally characterized by multiple pterygia that are found in the cervical, antecubital and popliteal regions. In this report, we present the treatment management of a 14-year-old case with late stage Escobar syndrome who was admitted due to multiple pterygia and bilateral knee contractures. The treatment of this case was conducted in collaboration with the department of orthopedics and the department of physical therapy. The treatment of the case was done in three stages: soft tissue procedures, femoral recurvatum osteotomy and triple arthrodesis, respectively. In addition to all these, the patient did intensive physical therapy for one year. As a result of the operations and physical therapy, adequate muscle strength was obtained.