JOURNAL OF ALLERGY AND CLINICAL IMMUNOLOGY, cilt.139, ss.1282-1292, 2017 (SCI İndekslerine Giren Dergi)
Background: X-linked hyper-IgM syndrome (XHIGM) is a primary immunodeficiency with high morbidity and mortality compared with those seen in healthy subjects. Hematopoietic cell transplantation (HCT) has been considered a curative therapy, but the procedure has inherent complications and might not be available for all patients.