Asymptomatic double aortic arch associated with tetralogy of Fallot (TOF) is a very rare congenital anomaly. Echocardiography plays a decisive role in the imaging of these patients as in several congenital heart diseases. In suspected double aortic arch diagnosis as in the current case, computed tomography or cardiac catheterization is of diagnostic importance for confirming complex anomalies such as this. In our case, these imaging techniques were performed and the patient underwent a one-stage total correction with ligation of an aortic arch via median sternotomy. Following an uneventful recovery, the patient was discharged on the postoperative fifth day.