Right ventricular endomyocardial fibrosis mimicking Ebstein anomaly in a patient with Behcet's disease: case report and review of the literature


Buturak A., SAYGILI Ö., Ulus S., Kalfa M. , Karabulut H., ALHAN C., ...More

MODERN RHEUMATOLOGY, vol.24, no.3, pp.532-536, 2014 (Journal Indexed in SCI) identifier identifier identifier

  • Publication Type: Article / Review
  • Volume: 24 Issue: 3
  • Publication Date: 2014
  • Doi Number: 10.3109/14397595.2013.874731
  • Title of Journal : MODERN RHEUMATOLOGY
  • Page Numbers: pp.532-536
  • Keywords: Behcet's disease, Endomyocardial fibrosis

Abstract

Behcet's disease is a multisystemic, chronic inflammatory disorder with diffuse clinical manifestations including the cardiovascular system. Endomyocardial fibrosis is a rarely seen complication of Behcet's disease leading to progressive heart failure. We report a case of right ventricular endomyocardial fibrosis mimicking Ebstein anomaly in a 26-year-old male Turkish patient with Behcet's disease, who had heart failure symptoms. In addition, the previously reported cases of endomyocardial fibrosis complicating Behcet's disease are reviewed in this article.