Inflammatory myofibroblastic tumor (IMT) is a rare benign neoplasm that consists of myofibroblastic spindle cells and inflammatory cells. It rarely emerges and affects central nervous system (CNS). CNS IMT has a high frequency of recurrence and malign transformation. There is no standard treatment protocol and response to steroid is often uncertain. In the article, a CNS IMT case where relapse is observed after resection with a response to steroids is represented.