Therapy resistant idiopathic scleredema: an underlying pathology not always present


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KALFA M., KOÇANAOĞULLARI H. , ZIHNI F. Y. , KARABULUT G. , EMMUNGİL H., İNAL V.

EUROPEAN JOURNAL OF RHEUMATOLOGY, vol.2, no.4, pp.163-0, 2015 (Journal Indexed in ESCI) identifier identifier

  • Publication Type: Article / Article
  • Volume: 2 Issue: 4
  • Publication Date: 2015
  • Doi Number: 10.5152/eurjrheum.2015.0004
  • Title of Journal : EUROPEAN JOURNAL OF RHEUMATOLOGY
  • Page Numbers: pp.163-0

Abstract

Scleredema is a rare connective tissue disorder of unknown pathogenesis. Three types of scleredema have been described, based on its association with postinfection, monoclonal gammopathy and diabetes mellitus. We report herein a case of scleredema which the diagnosis didn't get specified. The patient was followed regularly for 13 years and did not respond to various combinations of immuno-suppressants and psoralen plus ultraviolet A therapy. Treatment of scleredema is quite difficult and of limited success. At present, there is no proved treatment for this disease.